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Antibiotic strategies for eradicating Pseudomonas aeruginosa in people with cystic fibrosis
Antibiotics for treating acute chest syndrome in people with sickle cell disease
Antibiotics for treating community acquired pneumonia in people with sickle cell disease
New
Antibiotics for treating osteomyelitis in people with sickle cell disease (protocol stage)
Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis
New
Antioxidant micronutrients for lung disease in cystic fibrosis (protocol stage)
Appetite stimulants for people with cystic fibrosis (title stage)
Bisphosphonates for osteoporosis in people with cystic fibrosis
Blood transfusion for preventing stroke in people with sickle cell disease
Blood transfusions for acute chest syndrome in people with sickle cell disease (title stage)
Carnitine supplementation for treating people with inborn errors of metabolism (protocol stage)
Chemical pleurodesis versus surgical intervention for recurrent and persistent pneumothoraces in cystic fibrosis (title stage)
Chest physiotherapy compared to no chest physiotherapy for cystic fibrosis
Clotting factor concentrates given to prevent bleeding and bleeding-related complications in people with hemophilia A or B
Combination antimicrobial susceptibility testing for acute exacerbations in chronic infection of Pseudomonas aeruginosa in cystic fibrosis (protocol stage)
Conventional chest physiotherapy compared to other airway clearance techniques for cystic fibrosis
Deferasirox for iron chelation in people with transfusion-dependent thalassaemia (title stage)
Deferasirox for managing transfusional iron overload in people with sickle cell disease (title stage)
Desferrioxamine mesylate for managing transfusional iron overload in people with transfusion-dependent thalassaemia
Dietary advice for illness-related malnutrition in adults
Dietary interventions for phenylketonuria
Dietary treatment for familial hypercholesterolaemia
Disease modfying anti-rheumatic drugs in people with cystic fibrosis-related arthritis (title stage)
Dornase alpha for cystic fibrosis
Drug therapies for reducing gastric acidity in people with cystic fibrosis
Drugs for preventing red blood cell dehydration in people with sickle cell disease
New
Duration of intravenous antibiotic therapy in people with cystic fibrosis
Educational interventions for the self-management of cystic fibrosis in children and adolescents (title stage)
Elective versus symptomatic intravenous antibiotic therapy for cystic fibrosis
Updated
Enteral tube feeding for cystic fibrosis
Enzyme replacement therapy for Fabry disease (protocol stage)
Fluid replacement therapy for acute episodes of pain in people with sickle cell disease
Gene therapy for sickle cell disease (title stage)
Hematopoietic stem cell transplantation for children with sickle cell disease (protocol stage)
Hematopoietic stem cell transplantation for Gaucher disease (protocol stage)
Home intravenous antibiotics for cystic fibrosis
Hydroxyurea for sickle cell disease
Inhaled antibiotics for exacerbations in cystic fibrosis (title stage)
Inhaled antibiotics for pulmonary exacerbations in people with cystic fibrosis (title stage)
Inhaled bronchodilators for acute chest syndrome in people with sickle cell disease
Inhaled bronchodilators for cystic fibrosis
Inhaled corticosteroids for cystic fibrosis
Inhaled nitric oxide for acute chest syndrome in people with sickle cell disease
Inspiratory muscle training for cystic fibrosis (protocol stage)
Insulin and oral agents for managing cystic fibrosis-related diabetes
Macrolide antibiotics for cystic fibrosis
Macrolide antibiotics for cystic fibrosis (IPD Protocol) (title stage)
Nebulised anti-pseudomonal antibiotics for cystic fibrosis
Nebulised hypertonic saline for cystic fibrosis
Nebuliser devices for drug delivery in cystic fibrosis (title stage)
Neonatal screening for sickle cell disease
Newborn screening for cystic fibrosis
Non-invasive ventilation for cystic fibrosis
Omega-3 fatty acids (from fish oils) for cystic fibrosis
Once-daily versus multiple-daily dosing with intravenous aminoglycosides for cystic fibrosis
Oral anti-pseudomonal antibiotics for cystic fibrosis
Oral calorie supplements for cystic fibrosis
Oral deferiprone for iron chelation in people with thalassaemia
Oral non-steroidal anti-inflammatory drug therapy for cystic fibrosis
Oral protein calorie supplementation for children with chronic disease
Oral steroids for cystic fibrosis
Oscillating devices for airway clearance in people with cystic fibrosis (protocol stage)
Oxygen therapy for cystic fibrosis
Pharmacologic therapy for osteogenesis imperfecta (protocol stage)
Pharmacological agents (anti-inflammatory and analgesic) for managing symptoms in people with cystic fibrosis-related arthritis
Physical training for cystic fibrosis
Phytomedicines (medicines derived from plants) for sickle cell disease
Piracetam for reducing the incidence of painful sickle cell disease crises
Pneumococcal vaccines for sickle cell disease
Positive expiratory pressure physiotherapy for airway clearance in people with cystic fibrosis
Preoperative blood transfusions for sickle cell disease
Prophylactic anti-staphylococcal antibiotics for cystic fibrosis
Prophylactic antibiotics for preventing pneumococcal infection in children with sickle cell disease
Protein substitute for children and adults with phenylketonuria
Psychological interventions for people with cystic fibrosis and their families
Psychological therapies for sickle cell disease and pain
Psychological therapies for thalassaemia
Recombinant Factor VIIa concentrate versus plasma derived concentrates for the treatment of acute bleeding episodes in people with Haemophilia A and inhibitors
Recombinant growth hormone therapy for X-linked hypophosphatemia in children
Regular red blood cell transfusions for managing chronic chest complications in sickle cell disease (title stage)
Salmonella vaccine for preventing salmonella invasive infection in sickle cell disease (title stage)
Single versus combination intravenous antibiotic therapy for people with cystic fibrosis
Sodium channel blockers for cystic fibrosis
Splenectomy versus conservative management for acute sequestration crises in people with sickle cell disease
Statins for familial hypercholesterolemia in children (protocol stage)
New
Thiol derivatives for pulmonary disease in cystic fibrosis (protocol stage)
Topical cystic fibrosis transmembrane conductance regulator gene replacement for cystic fibrosis-related lung disease
Totally implantable vascular access devices for cystic fibrosis
Treatment for avascular necrosis of bone in people with sickle cell disease
Treatments for priapism in boys and men with sickle cell disease
Tyrosine supplementation for phenylketonuria
Ursodeoxycholic acid for cystic fibrosis-related liver disease
Vaccines for preventing infection with Pseudomonas aeruginosa in people with cystic fibrosis
Vaccines for preventing influenza in people with cystic fibrosis
Vaccines for preventing invasive salmonella infections in people with sickle cell disease (protocol stage)
Vitamin A supplementation for cystic fibrosis
Vitamin D supplementation for cystic fibrosis (title stage)